2006 ICD-9-CM Volume 1 Diagnosis Codes Home > Neoplasms 140-239 > Malignant Neoplasm Of Lymphatic And Hematopoietic Tissue 200-208 > Other Malignant Neoplasms Of Lymphoid And Histiocytic Tissue 202.* > 2006 ICD-9-CM Diagnosis 202.3 Malignant histiocytosis View the most recent version of ICD-9-CM 202.3 A rare, usually rapidly progressive disorder, characterized by abrupt onset, fever, weight loss, hepato-splenomegaly, pancytopenia, and lymphadenopathy. An aggressive Non-Hodgkin's adult lymphoma, comprised of two clinical syndromes: nasal T-cell lymphoma (previously called lethal midline granuloma) and pulmonary angiocentric B-cell lymphoma (previously called lymphomatoid granulomatosis). 202.3 is a non-specific code that cannot be used to specify a diagnosis 202.3 contains 5 index entries View the ICD-9-CM Volume 1 202.* hierarchy Alternate Terminology Histiocytic medullary reticulosis Malignant: reticuloendotheliosis reticulosis  Index entries containing 202.3: Histiocytosis (acute) (chronic) (subacute) 277.89 malignant (M9720/3) 202.3 Reticuloendotheliosis malignant (M9720/3) 202.3 Reticulosis (skin) histiocytic medullary (M9721/3) 202.3 malignant (M9720/3) 202.3 Sarcoma (M8800/3) - see also Neoplasm, connective tissue, malignant reticuloendothelial (M9720/3) 202.3